This abstract is assigned to sessions
| Title | Ocular findings revealing a Susac syndrome: a retrospective review of 4 cases |
| Accept poster if oral is not possible ? | Yes |
| Purpose | Our objective is to describe ocular findings and associated extraocular manifestations in Susac syndrome. |
| Methods | The charts of four patients (8 eyes) diagnosed with SUSAC syndrome were retrospectively reviewed. |
| Results | Mean age of our patients was 32 years (2 males and 2 females). The mean best corrected visual acuity was 20/32 (range, 20/63-20/20). Ocular findings at presentation were as follows: multiple branch retinal artery occlusions in 8 eyes, Gass plaques in 5 eyes, and segmental arteriolar wall hyperfluorescence on fluorescein angiography in 7 eyes. Ocular involvement was asymptomatic in 2 eyes, and subclinical in 3 eyes. Results of brain magnetic resonance imaging were abnormal in 3 patients. The audiogram showed sensorineural hearing loss in 2 patients. Treatment modalities included systemic corticosteroids (4 patients ; 100%), and cyclophosphamide (1 patient ; 25%). |
| Conclusion | Susac syndrome is a rare cause of occlusive retinal arteritis. Multiple branch retinal artery occlusions, Gass plaques and arteriolar wall hyperfluorescence on fluorescein angiography are highly suggestive of Susac syndrome. Association with encephalopathy and/or sensorineural hearing loss confirm the diagnosis. |
| Conflict of interest | No |
Author 1
| Last name | KHOCHTALI |
| Initials of first name(s) | S |
| Department | Department of Ophthalmology, Fattouma Bourguiba University Hospital |
| City | Monastir |
| Country | Tunisia |
Author 2
| Last name | Khairallah |
| Initials of first name(s) | M |
| Department | Susac syndrome is a rare cause of occlusive retinal arteritis. Multiple branch retinal artery occlus |
| City | Monastir |
| Country | Tunisia |
Author 3
| Last name | Smaoui |
| Initials of first name(s) | S |
| Department | Department of Ophthalmology, Fattouma Bourguiba University Hospital |
| City | Monastir |
| Country | Tunisia |
Author 4
| Last name | Ben Aoun |
| Initials of first name(s) | S |
| City | Monastir |
| Country | Tunisia |
Author 5
| Last name | Ben Yahia |
| Initials of first name(s) | S |
| Department | Department of Ophthalmology, Fattouma Bourguiba University Hospital |
| City | Monastir |
| Country | Tunisia |
Author 6
| Last name | Khairallah |
| Initials of first name(s) | M |
| Department | Department of Ophthalmology, Fattouma Bourguiba University Hospital |
| City | Monastir |
| Country | Tunisia |
