Familial exudative vitreoretinopathy simulating pars planitis
Accept poster if oral is not possible ?
Yes
Purpose
To describe a case of familial exudative vitreoretinopathy (FEVR) misdiagnosed as pars planitis.
Methods
Case Report
Results
An 11-year-old caucasian male patient with a history of strabismus in the right eye since the age of 3 presented 1 year ago with ocular hyperemia in the right eye and was evaluated by a retina specialist. The hypothesis of pars planitis was made and the patient underwent oral and systemic treatment with corticosteroids without improvement. His parents were non-consanguineous and there was no familial history of relevant ocular problems. His best correct visual acuity (BCVA) was 20/400 in the right eye (RE) and 20/20 in left eye (LE). The intraocular pressure (IOP) was 10 mmHg and biomicroscopy was normal in OU. The retina was attached in LE and temporal macular dragging could be seen bilaterally. There was tractional retinal detachment in RE involving the dystrophic macula temporally under thick epiretinal membranes. Fluorescent angiography (FA) disclosed important non-perfusion in the retinal periphery in OU. Ocular ultrasound did not demonstrate inflammatory or tumoral signs. Hemoglobin electrophoresis was requested, which was normal. The patient was treated with laser photocoagulation OU and evolved with preservation of visual acuity and maintenance of the attached retina without active neovascularization OU.
Conclusion
Neovascularization may be present intermediate uveitis. In these cases, it is necessary to assess whether there is in fact ocular inflammation and consider additional tests, especially angiography, which may reveal findings that suggest some entities over others. In case of FEVR, early treatment with photocoagulation can prevent more serious cases with retinal detachment and blindness.
Conflict of interest
No
1
Last name
ANDRADE
Initials of first name(s)
G
Department
Federal University of Sao Paulo
City
Sao Paulo
Country
Brazil
2
Last name
SIMEREN
Initials of first name(s)
N
Department
Federal University of Sao Paulo
City
Sao Paulo
Country
Brazil
3
Last name
FINAMOR
Initials of first name(s)
L
Department
Federal University of Sao Paulo
City
Sao Paulo
Country
Brazil
This website uses cookies to ensure you get the best experience on our website.
Learn more